Death Due to Complications of Anhidrotic Ectodermal Dysplasia

Ectodermal dysplasia comprises a group of disorders affecting ectodermal tissues. Severity depends on the genetic aberration; hyperpyrexia secondary to absence of sweat glands is a common complication. Treatment is supportive. This case report describes a 1‐month, 27‐day‐old male infant with a diagnosis of X‐linked recessive anhidrotic ectodermal dysplasia. On the day of his death, his mother swaddled him in a blanket and placed him on the couch at 5:30 am. When she picked him up at 8:00 am, he was unresponsive. At the emergency department, his rectal temperature was 40°C. Postmortem blood culture was positive for group B streptococcus, a possible etiology for fever. It is vital to teach parents that close monitoring of children with ectodermal dysplasia is necessary, as an increase in body temperature can become life threatening.     

Studying North Korea through North Korean migrants: lessons from the field

This article examines the use of North Korean defectors’ accounts as a source of information for studying the Democratic People’s Republic of Korea (DPRK). Information from defectors fills a vital knowledge gap and improves our understanding of North Korean politics, economics, and society. Witness accounts and interview data collected from people who were born in North Korea but have since left have been widely used by journalists, government agencies, international organizations, non-governmental organizations, and academics. There are, however, serious methodological issues in collecting, organizing, and interpreting information derived from defectors’ accounts. Selection and demographic biases, power relations between researchers and interviewees, monetary incentives, and language barriers are among those issues. We propose focus group discussions and participatory observation as complementary methods of data collection to mitigate the shortfalls of relying on individual interviews.     

环境群体性事件集体行动生成及消解:对典型个案的扎根分析

环境群体性事件一直秉持"污染侵害--群体施压"的逻辑框架,但与之相关的研究进路却忽略了对群体事件参与者内部动员、组织、集结及消解过程的分析。本文通过对大连"7·l6"海洋溢油事故后引发的渔民群体维权事件进行扎根分析发现,群体行动诱因、权变因素、群体行动共识形成、村庄网络化动员、集体行动生成、内部组织消解的核心范畴对环境群体性事件生成及消解有着显著影响,进而建构包含上述核心范畴的环境群体性事件参与者内部集结及消解路径模型,并阐释了模型中各因素内涵的相互关系。旨在研究结论对地方政府科学应对环境群体性事件具有一定的参考价值。     

基于抗原蛋白Fiber-2及细胞因子佐剂的Ⅰ群4型禽腺病毒亚单位疫苗的开发

为了开发一种抗I群4型禽腺病毒(FAd V-4)的亚单位疫苗,选择I群禽腺病毒血清4型流行毒株衣壳蛋白Fiber-2作为保护性抗原蛋白。利用昆虫细胞-杆状病毒系统生产Fiber-2蛋白,通过Westernblot检测重组蛋白的表达情况,利用双向琼脂扩散法检测重组Fiber-2的免疫原性。为了增强亚单位疫苗的免疫保护效果,添加鸡源白细胞介素2(chIL-2)和鸡源γ-干扰素(ch IFN-γ)作为免疫佐剂,与重组Fiber-2单独或混合使用,制备多种形式的亚单位疫苗,并进行动物攻毒保护试验。重组蛋白的Western-blot鉴定结果显示,63 ku处出现Fiber-2蛋白目的条带;双向琼脂扩散试验结果显示,重组蛋白效价达到1∶128,表现出良好的反应原性。动物攻毒保护试验结果显示,单独使用Fiber-2免疫SPF鸡,在50 μg/只的剂量下,可为SPF鸡提供100%的保护效果,以chIL-2和chIFN-γ为免疫佐剂,与重组Fiber-2联合免疫SPF鸡,可显著增强Fiber-2在低剂量(10 μg/只)下的免疫保护效果,上述结果表明重组Fiber-2联合chIL-2和chIFN-γ细胞因子佐剂所制备的亚单位疫苗在抗I群4型禽腺病毒感染领域具有良好的应用前景。     

我国跨境民族语言认同研究的现状与展望

语言认同是一种复杂的文化心理趋同现象,是其它认同的基础,深刻地影响着人们的语言行为。跨境民族的国家通用语认同、民族语认同和外语认同直接关系到国家发展战略、边疆民族地区社会安全稳定和民族语言文化的传承与保护。我国的跨境民族多,但国内学者关于跨境民族语言认同的研究还很少。基于现有语言认同研究相关文献,本文分析讨论了语言认同的基本概念和跨境民族语言认同研究现状,并提出了未来研究我国跨境民族语言认同的路径和建议。     

Good governance and differentiated integration: Graded membership in the European Union

The study of European integration has traditionally focused on organisational growth: the deepening and widening of the European Union (EU). By contrast, this article analyses organisational differentiation, a process in which states refuse, or are being refused, full integration but find value in establishing in‐between grades of membership. It describes how the EU's system of graded membership has developed, and it explains the positioning of states in this system. The core countries of the EU set a standard of ‘good governance’. The closer European countries are to this standard, the closer their membership grade is to the core. Some countries fall short of this standard and are refused further integration by the core: their membership grade increases with better governance. Other countries refuse further integration because they outperform the standards of the core countries: their membership grade decreases as governance improves. These conjectures are corroborated in a panel analysis of European countries.     

关于国有控股公司的几个问题

国有控股公司是政府作为国有资产所有代表行使其出资权利的中间层次。本对国有控股公司概念、分类、成因及组建方式进行了探讨,并提出了发展和完善国有控股公司所应注意的几个问题。     

谈网络群体性事件的成因及其防范

伴随着互联网的快速发展,网络已成为当今社会信息传播的主要媒介之一。网络群体性事件的发生与发展不仅迅猛,而且其事件的影响度和被关注度已非常之大,远远超出了人们对现实社会的群体性事件的把握与控制能力。因而,研究目前网络群体性事件的特点、成因,以及探讨网络群体性事件的防范策略,对疏导舆情、构建和谐社会具有重要的现实意义。     

化解群体性事件的对策

解决社会转型时期群体性事件要立足于国家长治久安的大局,在构筑和谐社会的进程中,实现对群体性事件的社会控制,为社会全面进步创造良好的条件。